Psychosocial aspects of cystic fibrosis

Basic aspects of cystic fibrosis.

Cystic fibrosis (CF) is manifestly a disease of the exocrine organs (1) to which the respiratory, digestive, and reproductive tracts are hereby included as honorary members. In years past, few individuals with CF survived infancy. Up to 10% of affected children died shortly after birth as a result of complications from meconium ileus, and survivors, who were typically malnourished, usually succ...

Adolescents with cystic fibrosis: psychosocial adjustment.

Patients aged between 12 and 16 years with cystic fibrosis were interviewed, as were their parents, to find out if psychosocial problems existed. All 27 of them appeared to be well adjusted and none had special problems at school; they were not socially isolated, and family relationships seemed to be good. Contributing factors were good communications patterns within the family and perhaps deni...

Immunological aspects on cystic fibrosis lung disease

Prevalence of Cystic Fibrosis Trans-membrane Conductance Regulator Gene common mutations in children with cystic fibrosis in Isfahan, Iran

Background: Cystic fibrosis (CF) is the most common lethal genetic disorder of Cystic Fibrosis Trans-membrane Conductance (CFTR) Regulator gene mutations. We aimed to investigate common mutations in CF patients and to assess its possible relationship with clinical presentations. Materials and Methods: This cross sectional study was conducted on 36 CF patients who were referred to a tertiary ped...

Aspects of bile acid metabolism in cystic fibrosis.

Goodchild, M. C., Murphy, G. M., Howell, A. MA, Nutter, S. A., Anderson, C. M. (1975). Archives of Disease in Childhood, 50, 769. Aspects of bile acid metabolism in cystic fibrosis. Previous reports have indicated that cystic fibrosis (CF) patients with pancreatic enzyme insufficiency have a raised faecal bile acid output. In this study, 18 out of 29 CF patients and 2 out of the 4 non-CF patien...